91精品少妇一区二区三区蜜桃臀,少妇搡BBBB搡BBB搡失恋,BBB片一毛片A片AA少妇,国产成人无码久久久久毛片朴信惠
掃碼關(guān)注公眾號(hào)           掃碼咨詢技術(shù)支持           掃碼咨詢技術(shù)服務(wù)
  
客服熱線:400-901-9800  客服QQ:4009019800  技術(shù)答疑  技術(shù)支持  質(zhì)量反饋  關(guān)于我們  聯(lián)系我們
96久久夜色精品国产九色杨思敏,国精产品久拍自产视频
Rabbit Anti-Junctophilin 3/Cy5.5 Conjugated antibody (bs-11083R-Cy5.5)
訂購熱線:400-901-9800
訂購郵箱:sales@bioss.com.cn
訂購QQ:  400-901-9800
技術(shù)支持:techsupport@bioss.com.cn
說 明 書: 100ul  
100ul/2980.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) bs-11083R-Cy5.5
英文名稱 Rabbit Anti-Junctophilin 3/Cy5.5 Conjugated antibody
中文名稱 Cy5.5標(biāo)記的連接蛋白JPH3抗體
別    名 JP-3; JP3; JPH3; JPH3_HUMAN; Junctophilin3; Junctophilin type 3; Junctophilin-3; TNRC22; Trinucleotide repeat-containing gene 22 protein.  
規(guī)格價(jià)格 100ul/2980元 購買        大包裝/詢價(jià)
說 明 書 100ul  
研究領(lǐng)域 心血管  神經(jīng)生物學(xué)  信號(hào)轉(zhuǎn)導(dǎo)  細(xì)胞粘附分子  
抗體來源 Rabbit
克隆類型 Polyclonal
交叉反應(yīng) (predicted: Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Zebrafish, Sheep, )
產(chǎn)品應(yīng)用 ICC=1:50-200 IF=1:50-200 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 81kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/ml
免 疫 原 KLH conjugated synthetic peptide derived from human Junctophilin 3
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
產(chǎn)品介紹 background:
Junctophilins are components of the junctional complexes between plasma membranes and endoplasmic or sarcoplasmic reticulums present in all excitable cells. Junctophilins contain a cytoplasmic domain which binds to the plasma membrane, as well as an ER/SR membrane spanning hydrophobic C-terminal segment. The three subtypes in this family are Junctophilin-1, -2 and -3. Junctophilin-1 is predominantly expressed in skeletal muscle, but is also expressed at low levels in heart. Junctophilin-2 is expressed in heart and skeletal muscle. Mutant mice lacking the Jph2 gene exhibit embryonic lethality and possess cardiac myocytes that express abnormal calcium transients. Junctophilin-3 is expressed in brain. The JPH3 alternatively spliced exon 2A has been suggested as a site for CTG repeat expansion leading to a Huntington disease-like autosomal dominant disorder.

Function:
Contributes to the stabilization of the junctional membrane complexes, which are common to excitable cells and mediate cross-talk between cell surface and intracellular ion channels. Probably acts by anchoring the plasma membrane and endoplasmic reticulum. May play an active role in certain neurons involved in motor coordination.

Subcellular Location:
Cell membrane. Endoplasmic reticulum membrane. Localized predominantly on the plasma membrane. The transmembrane domain is anchored in endoplasmic reticulum membrane, while the N-terminal part associates with the plasma membrane.

Tissue Specificity:
Specifically expressed in brain.

DISEASE:
Defects in JPH3 are the cause of Huntington disease-like type 2 (HDL2) [MIM:606438]. Huntington disease (HD) is a neurodegenerative disorder resulting primarily from the loss of medium spiny projection neurons in the striatum, especially in the caudate nucleus, and, to a lesser extent, atrophy of mesencephalic and cortical structures. The typical clinical picture of HD combines familial adult onset chorea and subcortical dementia that usually begin during the fourth decade of life.

Similarity:
Belongs to the junctophilin family. Contains 8 MORN repeats.

Database links:
UniProtKB/Swiss-Prot: Q8WXH2.2

Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
版權(quán)所有 2004-2026 www.rvdoil.com 北京博奧森生物技術(shù)有限公司
通過國際質(zhì)量管理體系ISO 9001:2015 GB/T 19001-2016    證書編號(hào): 00124Q34771R2M/1100
通過國際醫(yī)療器械-質(zhì)量管理體系ISO 13485:2016 GB/T 42061-2022    證書編號(hào): CQC24QY10047R0M/1100
京ICP備05066980號(hào)-1         京公網(wǎng)安備110107000727號(hào)
亚洲欧洲精品mv免费看 | 全免费一级毛片免费看无码播放 | 午夜成人电影免费在线 | 国内自拍真实伦在线观看 | 91人妻人人澡人人爽 | 久久精品人妻一区二区三区宅男必备 | 日本成人视频免费看片 | 精品人妻一区二区三区潮喷在线 | 17c.com少妇喷水 | 无码人妻精品1国产婷婷 | 国产亚洲色婷婷久久99 | 日本婬乱A片AAA毛片麻豆软件 | 无码一区二区三区av | 日本不卡视频在线播放 | 特级西西444www无码视频免费看 | 少妇搡BBBB搡BBB搡野外 | 午夜福利1000| 无码秘 人妻一区二区三区 熟妇高潮一区二区在线播放 | 天天AAA无码精品级 丝袜被扒在线观看网站 | 狠狠躁夜夜躁人人爽蜜桃 | 白丝 自慰到流白浆竹菊 | 无码人妻精品一桃在线看 | 亚洲铁杆无码在线观看视频 | 国产毛毛AAAAAAA做受 | 2019中文在线观看免费观看电视剧 | 日欧一片内射va在线影院 | 亚洲无码在线观看视频 | 麻豆精品国产传媒在线精品 | 成人视频在线观看久久 | 国产又爽 又黄 免费视频两年半 | 久密桃精品AV妻菠萝9 | 国产AⅤ一区仑乱羞羞哒哒 91丨九色丨丰满熟女首页 | 国产精品无码一区二区毛片视频 | 欲求不满五十路未亡人 | 污污污污污污污污在线观看视频 | 成人视频在线观看久久 | 国产乱妇乱子在线播放视频国产 | 国产小电影在线观看 | 91肥熟国产老肥熟女50p | 国产成人无码精品一区二区 | 91人妻人人人人爽 |