產(chǎn)品編號(hào) | bs-16128R |
英文名稱 | FLJ36733 Rabbit pAb |
中文名稱 | CCDC44/卷曲螺旋結(jié)構(gòu)域蛋白44抗體 |
別 名 | CCDC44; CDNA FLJ36733 fis; Coiled coil domain containing 44; Coiled-coil domain-containing protein 44; PRO0477; Taco1; TACO1_HUMAN; Translational activator of cytochrome c oxidase 1; Translational activator of mitochondrially-encoded cytochrome c oxidase I; UTERU2012856. |
研究領(lǐng)域 | 細(xì)胞生物 信號(hào)轉(zhuǎn)導(dǎo) 轉(zhuǎn)錄調(diào)節(jié)因子 線粒體 表觀遺傳學(xué) |
抗體來(lái)源 | Rabbit |
克隆類型 | Polyclonal |
交叉反應(yīng) | Rat (predicted: Human,Mouse,Rabbit,Sheep,Cow,Dog,Horse) |
產(chǎn)品應(yīng)用 | IHC-P=1:100-500,IHC-F=1:100-500,IF=1:100-500
not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
理論分子量 | 32 kDa |
檢測(cè)分子量 | |
細(xì)胞定位 | 細(xì)胞漿 線粒體 |
性 狀 | Liquid |
濃 度 | 1mg/ml |
免 疫 原 | KLH conjugated synthetic peptide derived from human FLJ36733: 51-150/297 |
亞 型 | |
純化方法 | affinity purified by Protein A |
緩 沖 液 | 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol. |
保存條件 | Shipped at 4℃. Store at -20℃ for one year. Avoid repeated freeze/thaw cycles. |
注意事項(xiàng) | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
PubMed | PubMed |
產(chǎn)品介紹 |
This gene encodes a mitochondrial protein that function as a translational activator of mitochondrially-encoded cytochrome c oxidase 1. Mutations in this gene are associated with Leigh syndrome.[provided by RefSeq, Mar 2010] Function: Acts as a translational activator of mitochondrially-encoded cytochrome c oxidase 1. Subcellular Location: Mitochondrion. DISEASE: Defects in TACO1 are a cause of Leigh syndrome (LS) [MIM:256000]. LS is a severe neurological disorder characterized by bilaterally symmetrical necrotic lesions in subcortical brain regions that is commonly associated with systemic cytochrome c oxidase (COX) deficiency. Similarity: Belongs to the TACO1 family. SWISS: Q9BSH4 Gene ID: 51204 Database links: Entrez Gene: 51204 Human Omim: 612958 Human SwissProt: Q9BSH4 Human Unigene: 174134 Human |
產(chǎn)品圖片 | |
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